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Case Reports

Abstract

Ossifying fasciitis is a rare, benign myofibroblastic neoplasm characterized by foci of metaplastic bone. This report describes a case of ossifying fasciitis to the superficial abdominal wall without a history of prior trauma or surgery, a rare location and history for this disease. A 37-year-old male presented with a four-month history of a firm, tender abdominal mass with no history of surgery or trauma to the area. Histopathology revealed a dermal-based tumor of spindled cells in a loose fascicular to storiform pattern within a myxoid stroma. Extensive calcification and ossification were observed, along with osteoclast-like cells. Immunohistochemical staining revealed strong smooth muscle actin staining in the tumoral cells. Analysis via fluorescence in situ hybridization demonstrated USP6 rearrangement. MRI showed an enhancing signal extending from the epidermis into the left external oblique muscle. Due to concern for herniation, the patient was referred to general surgery for excision. This case highlights a rare entity seen by dermatologists with a unique presentation, bringing awareness to this disease and its presentations.