Abstract:

Cutaneous collagenous vasculopathy (CCV) is a rarely occurring and recently described entity with less than 100 cases being reported in the literature since its inception in 2000. CCV is a microangiopathic process, predominantly affecting the superficial dermal vasculature, which clinically presents as a progressive development of blanching and symmetric telangiectasias arising on the lower extremities and spreading to the trunk and upper limbs. The exact etiology is poorly understand; however, associations with autoimmune conditions, cardiovascular disease, and diabetes have been reported. Herein we present a case of an adult female patient who presented with reticular, telangiectatic patches and scattered macules arising on the dorsal hands, abdomen, lower extremities, and lower back. The process was accompanied by increased bouts of erythema and a burning sensation after spending time in the sun. A biopsy was performed which demonstrated slightly ectatic and thickened blood vessels within the superficial dermis. Periodic acid-Schiff (PAS) staining highlighted the presence of amorphous material within the vasculature, corresponding to thickening. Given the histologic findings, a diagnosis of cutaneous collagenous vasculopathy was rendered. Our aim is to increase awareness of this rarely diagnosed entity, including its differential diagnostic mimickers, and possible approaches to management.

Financial Disclosure:
No current or relevant financial relationships exist.

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Alison Klenk